# ADAMTSL6β Protein Rescues Fibrillin-1 Microfibril Disorder in a Marfan Syndrome Mouse Model through the Promotion of Fibrillin-1 Assembly

**Type:** Papers  
**Canonical URL:** https://scholariq.org/papers/adamtsl6-protein-rescues-fibrillin-1-microfibril-disorder-in-a-marfan-syndrome/

## Facts

| Field | Value |
| --- | --- |
| Author Names | Masahiro Saito,Misaki Kurokawa,Masahito Oda,Masamitsu Oshima,Ko Tsutsui,Kazutaka Kosaka,Kazuhisa Nakao,Miho Ogawa,Ri-ichiroh Manabe,Naoto Suda,Ganjargal Ganburged,Yasunobu Hada,Toshihide Noguchi,Toshio Teranaka,Kiyotoshi Sekiguchi,Toshiyuki Yoneda,Takashi Tsuji |
| Citations | 55 |
| DOI | 10.1074/jbc.m111.243451 |
| Fields | Biochemistry, Genetics and Molecular Biology,Medicine |
| Open Access | true |
| OA Status | hybrid |
| OA URL | https://www.sciencedirect.com/science/article/pii/S0021925820507035/pdf |
| OpenAlex ID | https://openalex.org/W2129032853 |
| PMID | 21880733 |
| Type | article |
| Year | 2011 |

## Paper authors

- [Ko Tsutsui](https://scholariq.org/researchers/ko-tsutsui/)

## Paper primary topic

- [Connective tissue disorders research](https://scholariq.org/topics/connective-tissue-disorders-research/)

## Paper topics

- [Connective tissue disorders research](https://scholariq.org/topics/connective-tissue-disorders-research/)
- [Protease and Inhibitor Mechanisms](https://scholariq.org/topics/protease-and-inhibitor-mechanisms/)
- [Platelet Disorders and Treatments](https://scholariq.org/topics/platelet-disorders-and-treatments/)

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Source: ScholarIQ — public research metadata, principally OpenAlex. See https://scholariq.org/sources/ for provenance and https://scholariq.org/methodology/ for what these figures mean.