# Neuroinflammation, mitochondrial defects and neurodegeneration in mucopolysaccharidosis III type C mouse model

**Type:** Papers  
**Canonical URL:** https://scholariq.org/papers/neuroinflammation-mitochondrial-defects-and-neurodegeneration-in/

## Facts

| Field | Value |
| --- | --- |
| Author Names | C Martins,Helena Hůlková,Larbi Dridi,Virginie Dormoy-Raclet,Lubov Grigoryeva,Yoo Choi,Alex Langford-Smith,Fiona L. Wilkinson,Kazuhiro Ohmi,Graziella DiCristo,Édith Hamel,Jérôme Ausseil,David Cheillan,Alain Moreau,Eva Svobodová,Zuzana Hájková,Markéta Tesařová,Hana Hansíková,Brian Bigger,Martin Hřebı́ček,Alexey V. Pshezhetsky |
| Citations | 145 |
| DOI | 10.1093/brain/awu355 |
| Fields | Medicine |
| Open Access | true |
| OA Status | bronze |
| OA URL | https://academic.oup.com/brain/article-pdf/138/2/336/13798993/awu355.pdf |
| OpenAlex ID | https://openalex.org/W2046110239 |
| PMID | 25567323 |
| Type | article |
| Year | 2015 |

## Paper authors

- [David Cheillan](https://scholariq.org/researchers/david-cheillan/)

## Paper journal

- [Brain](https://scholariq.org/journals/brain/)

## Paper primary topic

- [Lysosomal Storage Disorders Research](https://scholariq.org/topics/lysosomal-storage-disorders-research/)

## Paper topics

- [Lysosomal Storage Disorders Research](https://scholariq.org/topics/lysosomal-storage-disorders-research/)
- [Glycogen Storage Diseases and Myoclonus](https://scholariq.org/topics/glycogen-storage-diseases-and-myoclonus/)
- [Trypanosoma species research and implications](https://scholariq.org/topics/trypanosoma-species-research-and-implications/)

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Source: ScholarIQ — public research metadata, principally OpenAlex. See https://scholariq.org/sources/ for provenance and https://scholariq.org/methodology/ for what these figures mean.
