# Bénédicte Neven

**Type:** Researchers  
**Canonical URL:** https://scholariq.org/researchers/benedicte-neven/

## Facts

| Field | Value |
| --- | --- |
| Citations | 25,166 |
| Field | Immunodeficiency and Autoimmune Disorders |
| h-index | 85 |
| i10-index | 275 |
| Last Known Institution | Université Paris-Panthéon-Assas |
| OpenAlex ID | https://openalex.org/A5006102363 |
| ORCID iD | https://orcid.org/0000-0001-8941-0935 |
| Works | 537 |

## Researcher papers

- [The European Society for Immunodeficiencies (ESID) Registry Working Definitions for the Clinical Diagnosis of Inborn Errors of Immunity](https://scholariq.org/papers/the-european-society-for-immunodeficiencies-esid-registry-working-definitions/)
- [A Modified γ-Retrovirus Vector for X-Linked Severe Combined Immunodeficiency](https://scholariq.org/papers/a-modified-retrovirus-vector-for-x-linked-severe-combined-immunodeficiency/)
- [Long-term outcome of Hurler syndrome patients after hematopoietic cell transplantation: an international multicenter study](https://scholariq.org/papers/long-term-outcome-of-hurler-syndrome-patients-after-hematopoietic-cell/)
- [Long-term follow-up of IPEX syndrome patients after different therapeutic strategies: An international multicenter retrospective study](https://scholariq.org/papers/long-term-follow-up-of-ipex-syndrome-patients-after-different-therapeutic/)
- [Preexisting autoantibodies to type I IFNs underlie critical COVID-19 pneumonia in patients with APS-1](https://scholariq.org/papers/preexisting-autoantibodies-to-type-i-ifns-underlie-critical-covid-19-pneumonia/)
- [Long‐term efficacy of the interleukin‐1 receptor antagonist anakinra in ten patients with neonatal‐onset multisystem inflammatory disease/chronic infantile neurologic, cutaneous, articular syndrome](https://scholariq.org/papers/long-term-efficacy-of-the-interleukin-1-receptor-antagonist-anakinra-in-ten/)
- [Mutations in <i>COPA</i> lead to abnormal trafficking of STING to the Golgi and interferon signaling](https://scholariq.org/papers/mutations-in-i-copa-i-lead-to-abnormal-trafficking-of-sting-to-the-golgi-and/)
- [Hematopoietic cell transplantation in chronic granulomatous disease: a study of 712 children and adults](https://scholariq.org/papers/hematopoietic-cell-transplantation-in-chronic-granulomatous-disease-a-study-of/)
- [Early-onset autoimmunity associated with SOCS1 haploinsufficiency](https://scholariq.org/papers/early-onset-autoimmunity-associated-with-socs1-haploinsufficiency/)
- [The CARD11-BCL10-MALT1 (CBM) signalosome complex: Stepping into the limelight of human primary immunodeficiency](https://scholariq.org/papers/the-card11-bcl10-malt1-cbm-signalosome-complex-stepping-into-the-limelight-of/)

## Researcher topics

- [Immunodeficiency and Autoimmune Disorders](https://scholariq.org/topics/immunodeficiency-and-autoimmune-disorders/)
- [Hematopoietic Stem Cell Transplantation](https://scholariq.org/topics/hematopoietic-stem-cell-transplantation/)
- [Inflammasome and immune disorders](https://scholariq.org/topics/inflammasome-and-immune-disorders/)
- [Immune Cell Function and Interaction](https://scholariq.org/topics/immune-cell-function-and-interaction/)
- [Blood disorders and treatments](https://scholariq.org/topics/blood-disorders-and-treatments/)

## Researcher university

- [Université Paris-Panthéon-Assas](https://scholariq.org/institutions/universite-paris-pantheon-assas/)

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Source: ScholarIQ — public research metadata, principally OpenAlex. See https://scholariq.org/sources/ for provenance and https://scholariq.org/methodology/ for what these figures mean.
