# Cystic Fibrosis Research Advances

**Type:** Topics  
**Canonical URL:** https://scholariq.org/topics/cystic-fibrosis-research-advances/

## Facts

| Field | Value |
| --- | --- |
| Description | This cluster of papers encompasses a wide range of topics related to cystic fibrosis, including therapeutic interventions, pulmonary infections, bronchiectasis, primary ciliary dyskinesia, mutation analysis, lung disease, microbiota, and nutrition management. The papers cover advancements in understanding the genetic and molecular basis of cystic fibrosis, as well as the development of novel treatments and management strategies. |
| Domain | Health Sciences |
| Field | Medicine |
| OpenAlex ID | t10665 |
| Works | 204 |

## Topic papers all

Showing 15 of 204.

- [Review on uremic toxins: Classification, concentration, and interindividual variability](https://scholariq.org/papers/review-on-uremic-toxins-classification-concentration-and-interindividual/)
- [A Longitudinal, Population-Based, Cohort Study of Childhood Asthma Followed to Adulthood](https://scholariq.org/papers/a-longitudinal-population-based-cohort-study-of-childhood-asthma-followed-to/)
- [European Respiratory Society guidelines for the management of adult bronchiectasis](https://scholariq.org/papers/european-respiratory-society-guidelines-for-the-management-of-adult/)
- [Cystic fibrosis: A worldwide analysis ofCFTR mutations?correlation with incidence data and application to screening](https://scholariq.org/papers/cystic-fibrosis-a-worldwide-analysis-ofcftr-mutations-correlation-with-incidence/)
- [Cystic Fibrosis Pulmonary Guidelines](https://scholariq.org/papers/cystic-fibrosis-pulmonary-guidelines/)
- [International Consensus Document (ICON): Common Variable Immunodeficiency Disorders](https://scholariq.org/papers/international-consensus-document-icon-common-variable-immunodeficiency-disorders/)
- [Morbidity and mortality in common variable immune deficiency over 4 decades](https://scholariq.org/papers/morbidity-and-mortality-in-common-variable-immune-deficiency-over-4-decades/)
- [Early Diagnosis of Cystic Fibrosis Through Neonatal Screening Prevents Severe Malnutrition and Improves Long-Term Growth](https://scholariq.org/papers/early-diagnosis-of-cystic-fibrosis-through-neonatal-screening-prevents-severe/)
- [International Union of Immunological Societies: 2017 Primary Immunodeficiency Diseases Committee Report on Inborn Errors of Immunity](https://scholariq.org/papers/international-union-of-immunological-societies-2017-primary-immunodeficiency/)
- [Cystic Fibrosis Pulmonary Guidelines: Treatment of Pulmonary Exacerbations](https://scholariq.org/papers/cystic-fibrosis-pulmonary-guidelines-treatment-of-pulmonary-exacerbations/)
- [Evidence-Based Practice Recommendations for Nutrition-Related Management of Children and Adults with Cystic Fibrosis and Pancreatic Insufficiency: Results of a Systematic Review](https://scholariq.org/papers/evidence-based-practice-recommendations-for-nutrition-related-management-of/)
- [Clinical Care Guidelines for Cystic Fibrosis–Related Diabetes](https://scholariq.org/papers/clinical-care-guidelines-for-cystic-fibrosis-related-diabetes/)
- [The European Society for Immunodeficiencies (ESID) Registry Working Definitions for the Clinical Diagnosis of Inborn Errors of Immunity](https://scholariq.org/papers/the-european-society-for-immunodeficiencies-esid-registry-working-definitions/)
- [Global and regional risk of disabling sequelae from bacterial meningitis: a systematic review and meta-analysis](https://scholariq.org/papers/global-and-regional-risk-of-disabling-sequelae-from-bacterial-meningitis-a/)
- [Rare Disease Terminology and Definitions—A Systematic Global Review: Report of the ISPOR Rare Disease Special Interest Group](https://scholariq.org/papers/rare-disease-terminology-and-definitions-a-systematic-global-review-report-of/)

## Topic primary papers

Showing 15 of 106.

- [European Respiratory Society guidelines for the management of adult bronchiectasis](https://scholariq.org/papers/european-respiratory-society-guidelines-for-the-management-of-adult/)
- [Cystic fibrosis: A worldwide analysis ofCFTR mutations?correlation with incidence data and application to screening](https://scholariq.org/papers/cystic-fibrosis-a-worldwide-analysis-ofcftr-mutations-correlation-with-incidence/)
- [Cystic Fibrosis Pulmonary Guidelines](https://scholariq.org/papers/cystic-fibrosis-pulmonary-guidelines/)
- [Early Diagnosis of Cystic Fibrosis Through Neonatal Screening Prevents Severe Malnutrition and Improves Long-Term Growth](https://scholariq.org/papers/early-diagnosis-of-cystic-fibrosis-through-neonatal-screening-prevents-severe/)
- [Cystic Fibrosis Pulmonary Guidelines: Treatment of Pulmonary Exacerbations](https://scholariq.org/papers/cystic-fibrosis-pulmonary-guidelines-treatment-of-pulmonary-exacerbations/)
- [Evidence-Based Practice Recommendations for Nutrition-Related Management of Children and Adults with Cystic Fibrosis and Pancreatic Insufficiency: Results of a Systematic Review](https://scholariq.org/papers/evidence-based-practice-recommendations-for-nutrition-related-management-of/)
- [Clinical Care Guidelines for Cystic Fibrosis–Related Diabetes](https://scholariq.org/papers/clinical-care-guidelines-for-cystic-fibrosis-related-diabetes/)
- [Cystic Fibrosis Pulmonary Guidelines](https://scholariq.org/papers/cystic-fibrosis-pulmonary-guidelines-2/)
- [Specific Lipopolysaccharide Found in Cystic Fibrosis Airway <i>Pseudomonas aeruginosa</i>](https://scholariq.org/papers/specific-lipopolysaccharide-found-in-cystic-fibrosis-airway-i-pseudomonas/)
- [Guidelines for the physiotherapy management of the adult, medical, spontaneously breathing patient](https://scholariq.org/papers/guidelines-for-the-physiotherapy-management-of-the-adult-medical-spontaneously/)
- [Clinical outcome after early Pseudomonas aeruginosa infection in cystic fibrosis](https://scholariq.org/papers/clinical-outcome-after-early-pseudomonas-aeruginosa-infection-in-cystic-fibrosis/)
- [Acceleration of lung disease in children with cystic fibrosis after Pseudomonas aeruginosa acquisition](https://scholariq.org/papers/acceleration-of-lung-disease-in-children-with-cystic-fibrosis-after-pseudomonas/)
- [Effect of genotype on phenotype and mortality in cystic fibrosis: a retrospective cohort study](https://scholariq.org/papers/effect-of-genotype-on-phenotype-and-mortality-in-cystic-fibrosis-a-retrospective/)
- [Nutritional Benefits of Neonatal Screening for Cystic Fibrosis](https://scholariq.org/papers/nutritional-benefits-of-neonatal-screening-for-cystic-fibrosis/)
- [The origin of the major cystic fibrosis mutation (ΔF508) in European populations](https://scholariq.org/papers/the-origin-of-the-major-cystic-fibrosis-mutation-f508-in-european-populations/)

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Source: ScholarIQ — public research metadata, principally OpenAlex. See https://scholariq.org/sources/ for provenance and https://scholariq.org/methodology/ for what these figures mean.