Prion Diseases and Protein Misfolding

TopicLeading institutions, researchers & key papers

This cluster of papers focuses on the causes, molecular basis, detection, transmission, and potential treatments for prion diseases, including variant Creutzfeldt-Jakob disease. It explores the role of infectious prions, protein misfolding, and their impact on neurodegenerative diseases. The research also delves into the pathology of these diseases and their transmissibility through blood transfusion.

Works

IDs:OpenAlex

How has Prion Diseases and Protein Misfolding's publication output changed over time?

ScholarIQpublication output · 2007–2022

Output declined50% over the shown period — from 2 works in 2007 to 1 in 2022.

2007201020132015201620172019202020212022

What are the most-cited papers on Prion Diseases and Protein Misfolding?

ScholarIQmost cited works

Mutations in prion-like domains in hnRNPA2B1 and hnRNPA1 cause multisystem proteinopathy and ALS

Hong Joo Kim, Nam Chul Kim, Yong‐Dong Wang, Emily A. Scarborough, Jennifer C. Moore, Zamia Diaz, Kyle S. MacLea, Brian D. Freibaum, Songqing Li, Amandine Molliex, Anderson Kanagaraj, Robert Carter, Khrista Boylan, Aleksandra Wojtas, Rosa Rademakers, Jack L. Pinkus, Steven A. Greenberg, John Q. Trojanowski, Bryan J. Traynor, Bradley Smith, Simon Topp, Athina-Soragia Gkazi, Jack W. Miller, Christopher E. Shaw, Michael Kottlors, Janbernd Kirschner, Alan Pestronk, Yun R. Li, Alice F. Ford, Aaron D. Gitler, Michael Benatar, Oliver D. King, Virginia Kimonis, Eric D. Ross, Conrad C. Weihl, James Shorter, J. Paul Taylor

Nature. 20131,517 CitationsOPEN ACCESS

Diagnostic Value of Cerebrospinal Fluid Neurofilament Light Protein in Neurology

Claire Bridel, Wessel N. van Wieringen, Henrik Zetterberg, Betty M. Tijms, Charlotte E. Teunissen, and the NFL Group, José C. Álvarez‐Cermeño, Ulf Andréasson, Markus Axelsson, David Bäckström, Aleš Bartoš, Maria Bjerke, Kaj Blennow, Adam L. Boxer, Lou Brundin, Joachim Burman, Tove Christensen, L Fialová, Lars Forsgren, Jette Lautrup Frederiksen, Magnus Gisslén, Elizabeth Gray, Martin Gunnarsson, Sara Hall, Oskar Hansson, Megan K. Herbert, Joel Jakobsson, Jan Jessen-Krut, Shorena Janelidze, Gudmundur Johannsson, Michael Jonsson, Ludwig Kappos, Mohsen Khademi, Michael Khalil, Jens Kühle, Mikael Landén, Ville Leinonen, Giancarlo Logroscino, Ching‐Hua Lu, Jan Lycke, Nadia Magdalinou, Andrea Malaspina, Niklas Mattsson, Lieke Meeter, Sanjay R. Mehta, Signe Modvig, Tomas Olsson, Ross W. Paterson, Josué Pérez‐Santiago, Fredrik Piehl, Yolande A.L. Pijnenburg, Okko T. Pyykkö, Óskar Ragnarsson, Julio C. Rojas, Jeppe Romme Christensen, Linda Sandberg, Carole Scherling, Jonathan M. Schott, Finn Sellebjerg, Isabella Laura Simone, Tobias Skillbäck, Morten Stilund, Peter Sundström, Anders Svenningsson, Rosanna Tortelli, Carla Tortorella, Alessandro Trentini, Maria Troiano, Martin R. Turner, John C. van Swieten, Mattias Vågberg, Marcel M. Verbeek, Luisa María Villar, Pieter Jelle Visser, Anders Wallin, Andreas Weiss, Carsten Wikkelsø, Edward J. Wild

JAMA Neurology. 2019777 CitationsOPEN ACCESS

Complete structure of the glycosyl phosphatidylinositol membrane anchor of rat brain Thy-1 glycoprotein

Steve W. Homans, Michael A. J. Ferguson, Raymond A. Dwek, Thomas W. Rademacher, R. Anand, Abigail Williams

Nature. 1988448 Citations

Biomarkers and diagnostic guidelines for sporadic Creutzfeldt-Jakob disease

Péter Hermann, Brian S. Appleby, Jean‐Philippe Brandel, Byron Caughey, Steven Collins, Michael D. Geschwind, Alison Green, Stéphane Haı̈k, Gábor G. Kovács, Anna Ladogana, Franc Llorens, Simon Mead, Noriyuki Nishida, Suvankar Pal, Piero Parchi, Maurizio Pocchiari, Katsuya Satoh, Gianluigi Zanusso, Inga Zerr

S70053155. 2021349 CitationsOPEN ACCESS

Interaction of Cellular Prion and Stress-Inducible Protein 1 Promotes Neuritogenesis and Neuroprotection by Distinct Signaling Pathways

Marilene H. Lopes, Glaucia N. M. Hajj, Angelita Muras, Gabriel. L Mancini, Rosa M. P. S. Castro, Karina Braga Ribeiro, Helena Brentani, Rafael Linden, Vilma R. Martins

Journal of Neuroscience. 2005280 CitationsOPEN ACCESS